Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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Churchill livingstone ; New York. Neuroimaging studies revealed diffuse or localized thickening of the dura, and MRI findings were key to diagnosis of this disorder.

Eur J Radiol ; It was first described by Charcot and later by Naffziger and Stern.

This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3. Fungal and AFB culture were negative. Click on image for details.

Report of three cases. Idiopathic hypertrophic cranial pachymeningitis. MR imaging of the meninges.

Inflammatory hypertrophic cranial pachymeningitis. Author information Article notes Copyright and License information Disclaimer. Idiopathic hypertrophic cranial pachymeningitis: Varied manifestations of a single disease entity.


Idiopathic hypertrophic pachymeningitis.

Long term improvement of idiopathic hypertrophic cranial pachymeningitis by lymphocytapheresis. How to cite this URL: Please review our privacy policy. No Shinkei Geka ; This article has been cited by other articles in PMC.

A succesful case of hypertrophic cranial pachymeningitis treated with optic nerve decompression. Clin Exp Neurol ; Hypertrophic pachymeningitis is a rare form of diffuse inflammatory disease that causes thickening of the dura mater.

Idiopathic hypertrophic pachymeningitis.

National Center for Biotechnology InformationU. An unusual cause of subacute and chronic headache.

Magnetic resonance imaging MRI of the brain showed diffuse enhancement with thickening of the pxchymeningitis. How to cite this article: Combined therapy of corticosteroid and azathioprine in hypertrophic cranial pachymeningitis. Case 1 Case 1.

N KarthikK. Optic neuropathy associated with hypertrophic cranial pachymeningitis.

Exact etiopathogenesis of this entity is still unknown, but it is speculated to be an autoimmune phenomenon or occur as a direct result of infectious or infiltrative pathology. Idiopathic hypertrophic chronic pachymeningitis presenting with acute visual loss. When no cause is identified it is termed idiopathic hypertrophic pachymeningitis. All patients were treated with corticosteroid and improved intially, but half of them experienced relapses.


Articles Cases Courses Quiz. Open pachmeningitis journal indexed with Index Medicus. Idiopathic hypertrophic cranial pachymeningitis: Rheumatoid factor positive hypertrophic cranial pachymeningitis in association with hypopituitarism and multiple cranial nerve palsies.

Hypertrophic pachymeningitis

Pathological examination in two autopsied cases revealed diffuse thickening of the dura, especially in the posterior part of the falx cerebri and the tentorium cerebelli. Recurrent cranial neuropathy as a clinical presentation of idiopathic inflammation of the duramater: Cerebrospinal fluid analysis revealed normal cell count, protein and sugar levels.

Tuberculous hypertrophic pachymeningitis involving the posterior fossa and high cervical hhypertrophic. Axial section of MRI image showing diffuse enhacement with thickening of meninges.